A Rare Case of Nasal Polyposis in Hurler Syndrome
Published: 2023-07-17
Page: 342-345
Issue: 2023 - Volume 6 [Issue 2]
W. Lendoye *
ENT Head and Neck Surgery Department, Ibn Rochd University Hospital, Casablanca, Morocco.
S. Moujrid
ENT Head and Neck Surgery Department, Ibn Rochd University Hospital, Casablanca, Morocco.
Y. Oukessou
ENT Head and Neck Surgery Department, Ibn Rochd University Hospital, Casablanca, Morocco.
R. Abada
ENT Head and Neck Surgery Department, Ibn Rochd University Hospital, Casablanca, Morocco.
M. Mahtar
ENT Head and Neck Surgery Department, Ibn Rochd University Hospital, Casablanca, Morocco.
*Author to whom correspondence should be addressed.
Abstract
Mucopolysaccharidosis (MPS) type I is a rare multisystem disorder resulting from the accumulation of breakdown products of glycosaminoglycans in the body tissues. Many patients with this disease undergo ENT surgeries as adenotonsillectomy. Nasal polyposis is a rare occurrence.
The aim of this work is to present a very rare association observed in an 8-years-old patient with Hurler syndrome treated in the ENT Head and Neck Surgery department of Ibn Rochd University Hospital Casablanca, for nasal polyposis and adenoid hypertrophy.
Keywords: Mucopolysaccharidosis (MPS) I, glycosaminoglycan (GAG), nasal polyps