Unveiling Type 4A Choledochal Cyst a Congenital Anomaly Presenting in Adulthood: A Surgical Challenge

Shrikanta Biswas *

SCB Medical College and Hospital, Cuttack, Odisha, India.

*Author to whom correspondence should be addressed.


Abstract

Rare congenital biliary tree malformations known as choledochal cysts can have a substantial negative impact on morbidity and mortality if they are not detected and treated promptly. The dilatation of either the intrahepatic or extrahepatic bile ducts, or both, is a characteristic of these cysts. Asian populations are more likely to have choledochal cysts; in Japan, the frequency is as high as one in per 1000 live births. There are 5 subtypes of choledochal cyst and in adults type 4 is the most common. Here we report a case of a 52-year-old lady who presented with vague abdominal pain and on evaluation was incidentally found to have a choledochal cyst type 4A. The patient underwent excision of the extrahepatic hugely dilated choledochal cyst with cholecystectomy and reconstruction was done by Roux-en-Y hepaticojejunostomy to the confluence of the right and left hepatic duct at the hilum.

Keywords: Choledochal cyst, todani, hepaticojejunostomy, liver transplant, hepatectomy, Roux-en-Y, choledochocele, diverticulum, pancreatic divisum


How to Cite

Biswas, Shrikanta. 2024. “Unveiling Type 4A Choledochal Cyst a Congenital Anomaly Presenting in Adulthood: A Surgical Challenge”. Asian Journal of Case Reports in Surgery 7 (2):352-59. https://journalajcrs.com/index.php/AJCRS/article/view/549.

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