A Rare Case Presentation of Chondromyxoid Fibroma Involving the Sphenoid Sinus
Published: 2024-02-29
Page: 100-108
Issue: 2024 - Volume 7 [Issue 1]
F. El Mourabit *
Department of Otolaryngology, Head and Neck Surgerya, University Hospital Ibn Rochd, Casablanca, Morocco.
C. Rsaissi
Department of Otolaryngology, Head and Neck Surgerya, University Hospital Ibn Rochd, Casablanca, Morocco.
M. Loudghiri
Department of Otolaryngology, Head and Neck Surgerya, University Hospital Ibn Rochd, Casablanca, Morocco.
W. Bijou
Department of Otolaryngology, Head and Neck Surgerya, University Hospital Ibn Rochd, Casablanca, Morocco.
Y. Oukessou
Department of Otolaryngology, Head and Neck Surgerya, University Hospital Ibn Rochd, Casablanca, Morocco.
S. Rouadi
Department of Otolaryngology, Head and Neck Surgerya, University Hospital Ibn Rochd, Casablanca, Morocco.
R. Abada
Department of Otolaryngology, Head and Neck Surgerya, University Hospital Ibn Rochd, Casablanca, Morocco.
M. Roubal
Department of Otolaryngology, Head and Neck Surgerya, University Hospital Ibn Rochd, Casablanca, Morocco.
M. Mahtar
Department of Otolaryngology, Head and Neck Surgerya, University Hospital Ibn Rochd, Casablanca, Morocco.
*Author to whom correspondence should be addressed.
Abstract
Chondromyxoid fibroma (CMF) is an uncommon benign tumor of chondroid, myxoid and fibrous tissues. It is a rare bone tumor found mainly in long bones, so its presence at the base of the skull is particularly rare. The presence of monoclonal gammopathy of minor significance (MGUS) prompted the consideration and investigation of a plasma cell disorder. We describe the diagnosis and treatment of a 47-year-old female patient with a large CMF originating from the sphenoid sinus. However, chondromyxoid fibroma was correctly diagnosed based on CT and MRI results and a biopsy.
Keywords: Chondromyxoid fibroma, sphenoid sinus, CT, magnetic resonance imaging, monoclonal gammopathy of undetermined significance